Includes bibliographical references and index.

Embryology and development of the ductal plate / Clifford W. Bogue -- Cholangiocyte biology as relevant to cystic liver diseases / Silvia Lecchi ... [and others] -- Cholangiocyte cilia and basal bodies / Tatyana V. Masyuk, Anatoliy I. Masyuk, and Nicholas F. LaRusso -- Genetics of fibrocystic diseases of the liver and molecular approaches to therapy / Maya Tuchman, William A. Gahl, and Meral Gunay-Aygun -- Radiologic findings in the fibrocystic diseases / Orpheus Kolokythas and Grace Phillips -- Pathology of fibrocystic diseases of the liver / Camtu D. Nguyen Truong and Matthew M. Yeh -- Alagille Syndrome and JAGGED1/NOTCH sequence / Binita M. Kamath, Kathleen M. Loomes, and David A Piccoli -- Biliary atresia and the ductal plate / Ronald J. Sokol and Cara L. Mack
Nephronophthisis and renal-hepatic-pancreatic dysplasia of Ivemark / David A. Myers and Jordan M. Symons -- Meckel and Joubert syndromes / Melissa A. Parisi, Laura S. Finn, and Ian A. Glass -- Bardet-Biedl and Jeune syndromes / Aoife M. Waters and Philip L Beales -- Congenital disorders of glycosylation and their effects on the liver / Erik A. Eklund and Hudson H. Freeze -- Autosomal recessive polycystic kidney disease / Jodi M. Smith and Ruth A. McDonald -- Caroli disease, Caroli syndrome, and Congenital hepatic fibrosis / Ronen Arnon, Henrietta Kotlus Rosenberg, and Frederick J. Suchy -- Simple hepatic cysts/choledochal cysts / André A.S. Dick and Patrick J. Healey -- Autosomal dominant polycystic liver disease / Qi Qian, Vicente E. Torres, and Stefan Somlo -- Echinococcal/Hydatid cysts of the liver / Paul S. Pottinger, Austin Spitzer, and Raymond R. Yeung -- Miscellaneous cystic lesions of the liver / Iris W. Liou -- Vascular complications of fibrocystic liver disease / Maarouf Hoteit and Patrick S. Kamath -- Biliary cystadenoma and cystadenocarcinoma / Paolo Del Poggio, Ezio Pezzica, and Daniela Corti -- Cholangitis / Shayan Irani and Richard Kozarek -- Surgical management of fibrocystic liver disease / Meelie DebRoy

In recent years, there have been huge advances in the understanding of the genetic and molecular basis of the fibrocystic diseases. This volume provides a thorough review of fibrocyctic diseases that affect the liver. It contains in-depth discussions of the genetics, molecular biology, pathogenesis, histology, clinical presentations, complications of, treatment, and prognosis of the conditions affecting children and adults, and hence will be the gold-standard reference for these conditions. In addition, the histological features that distinguish these conditions from other potentially fibrosin